von Gierke disease
Billable / specificHCC V28 50
E74.01 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Type I glycogen storage disease
Includes (from E74)
- Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Excludes1
Not coded here — never report together with this code.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74) (from E74)
- androgen insensitivity syndrome (E34.5-) (from E74)
- congenital adrenal hyperplasia (E25.0) (from E74)
- hemolytic anemias attributable to enzyme disorders (D55.-) (from E74)
- Marfan syndrome (Q87.4-) (from E74)
- 5-alpha-reductase deficiency (E29.1) (from E74)
- diabetes mellitus (E08-E13) (from E74)
- hypoglycemia NOS (E16.2) (from E74)
- increased secretion of glucagon (E16.3) (from E74)
- mucopolysaccharidosis (E76.0-E76.3) (from E74)
Excludes2
Not included here — may be reported together when both conditions exist.
Also known as
- Type I glycogen storage disease
- Deficiency, deficient, glucose-6-phosphatase
- Disease, diseased, Gierke's
- Disease, diseased, glycogen storage, glucose-6-phosphatase deficiency
- Disease, diseased, glycogen storage, type I
- Disease, diseased, glycogen storage, Von Gierke's
- Disease, diseased, van Creveld-von Gierke
- Disease, diseased, von Gierke's
- Gierke's disease
- Van Creveld-von Gierke disease
- Von Gierke's disease
Parent code
- E74.0Glycogen storage diseaseHeader