Periodic fever syndromes
Billable / specificHCC V28 94
M04.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Familial Mediterranean fever
- Hyperimmunoglobin D syndrome
- Mevalonate kinase deficiency
- Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
Includes (from M04)
- Note: Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
Excludes2
Not included here — may be reported together when both conditions exist.
- arthropathic psoriasis (L40.5-) (from M04)
- certain conditions originating in the perinatal period (P04-P96) (from M04)
- certain infectious and parasitic diseases (A00-B99) (from M04)
- compartment syndrome (traumatic) (T79.A-) (from M04)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from M04)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) (from M04)
- endocrine, nutritional and metabolic diseases (E00-E88) (from M04)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from M04)
- neoplasms (C00-D49) (from M04)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from M04)
- Crohn's disease (K50.-) (from M04)
Also known as
- Familial Mediterranean fever
- Hyperimmunoglobin D syndrome
- Mevalonate kinase deficiency
- Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
- Arthritis, arthritic, in Mediterranean fever, familial
- Deficiency, deficient, mevalonate kinase
- Fever, Mediterranean, familial
- Fever, periodic
- Mediterranean, fever, familial
- Syndrome, hyperimmunoglobulin D
- Syndrome, periodic fever
- Syndrome, tumor necrosis factor receptor associated periodic
- TRAPS
Parent code
- M04Autoinflammatory syndromesHeader