Cryopyrin-associated periodic syndromes
Billable / specificHCC V28 94
M04.2 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
- Familial cold autoinflammatory syndrome
- Familial cold urticaria
- Muckle-Wells syndrome
- Neonatal onset multisystemic inflammatory disorder [NOMID]
Includes (from M04)
- Note: Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
Excludes2
Not included here — may be reported together when both conditions exist.
- arthropathic psoriasis (L40.5-) (from M04)
- certain conditions originating in the perinatal period (P04-P96) (from M04)
- certain infectious and parasitic diseases (A00-B99) (from M04)
- compartment syndrome (traumatic) (T79.A-) (from M04)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from M04)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) (from M04)
- endocrine, nutritional and metabolic diseases (E00-E88) (from M04)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from M04)
- neoplasms (C00-D49) (from M04)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from M04)
- Crohn's disease (K50.-) (from M04)
Also known as
- Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
- Familial cold autoinflammatory syndrome
- Familial cold urticaria
- Muckle-Wells syndrome
- Neonatal onset multisystemic inflammatory disorder [NOMID]
- CINCA
- Disorder, neonatal onset multisystemic inflammatory
- NOMID
- Syndrome, chronic, infantile neurological, cutaneous and articular
- Syndrome, cryopyrin-associated periodic
- Syndrome, familial cold autoinflammatory
- Syndrome, Muckle-Wells
- Urticaria, familial cold
Parent code
- M04Autoinflammatory syndromesHeader