VEXAS syndrome
Billable / specificNew in FY2027
M04.3 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Inclusion terms
Applicable to
- Vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic syndrome
Includes (from M04)
- Note: Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
Excludes2
Not included here — may be reported together when both conditions exist.
- arthropathic psoriasis (L40.5-) (from M04)
- certain conditions originating in the perinatal period (P04-P96) (from M04)
- certain infectious and parasitic diseases (A00-B99) (from M04)
- compartment syndrome (traumatic) (T79.A-) (from M04)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from M04)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) (from M04)
- endocrine, nutritional and metabolic diseases (E00-E88) (from M04)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from M04)
- neoplasms (C00-D49) (from M04)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from M04)
- Crohn's disease (K50.-) (from M04)
Code also
An additional code may be needed.
- any associated conditions
Also known as
- Vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic syndrome
- Syndrome, vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic
- Syndrome, VEXAS
Parent code
- M04Autoinflammatory syndromesHeader