D76.1

Hemophagocytic lymphohistiocytosis

Billable / specificHCC V28 115

D76.1 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Not coded here — never report together with this code.

(Abt-) Letterer-Siwe disease (C96.0) (from D76)
eosinophilic granuloma (C96.6) (from D76)
Hand-Schüller-Christian disease (C96.5) (from D76)
histiocytic medullary reticulosis (C96.9) (from D76)
histiocytic sarcoma (C96.A) (from D76)
histiocytosis X, multifocal (C96.5) (from D76)
histiocytosis X, unifocal (C96.6) (from D76)
Langerhans-cell histiocytosis, multifocal (C96.5) (from D76)
Langerhans-cell histiocytosis NOS (C96.6) (from D76)
Langerhans-cell histiocytosis, unifocal (C96.6) (from D76)
leukemic reticuloendotheliosis (C91.4-) (from D76)
lipomelanotic reticulosis (I89.8) (from D76)
malignant histiocytosis (C96.A) (from D76)
malignant reticulosis (C86.0) (from D76)
nonlipid reticuloendotheliosis (C96.0) (from D76)

Not included here — may be reported together when both conditions exist.

autoimmune disease (systemic) NOS (M35.9) (from D76)
certain conditions originating in the perinatal period (P00-P96) (from D76)
complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D76)
congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D76)
endocrine, nutritional and metabolic diseases (E00-E88) (from D76)
human immunodeficiency virus [HIV] disease (B20) (from D76)
injury, poisoning and certain other consequences of external causes (S00-T88) (from D76)
neoplasms (C00-D49) (from D76)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D76)

D76Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissueHeader