D76.3

Other histiocytosis syndromes

Billable / specificHCC V28 115

D76.3 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.

Inclusion terms

Applicable to

  • Reticulohistiocytoma (giant-cell)
  • Sinus histiocytosis with massive lymphadenopathy
  • Xanthogranuloma

Excludes1

Not coded here — never report together with this code.

  • (Abt-) Letterer-Siwe disease (C96.0) (from D76)
  • eosinophilic granuloma (C96.6) (from D76)
  • Hand-Schüller-Christian disease (C96.5) (from D76)
  • histiocytic medullary reticulosis (C96.9) (from D76)
  • histiocytic sarcoma (C96.A) (from D76)
  • histiocytosis X, multifocal (C96.5) (from D76)
  • histiocytosis X, unifocal (C96.6) (from D76)
  • Langerhans-cell histiocytosis, multifocal (C96.5) (from D76)
  • Langerhans-cell histiocytosis NOS (C96.6) (from D76)
  • Langerhans-cell histiocytosis, unifocal (C96.6) (from D76)
  • leukemic reticuloendotheliosis (C91.4-) (from D76)
  • lipomelanotic reticulosis (I89.8) (from D76)
  • malignant histiocytosis (C96.A) (from D76)
  • malignant reticulosis (C86.0) (from D76)
  • nonlipid reticuloendotheliosis (C96.0) (from D76)

Excludes2

Not included here — may be reported together when both conditions exist.

  • autoimmune disease (systemic) NOS (M35.9) (from D76)
  • certain conditions originating in the perinatal period (P00-P96) (from D76)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D76)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D76)
  • endocrine, nutritional and metabolic diseases (E00-E88) (from D76)
  • human immunodeficiency virus [HIV] disease (B20) (from D76)
  • injury, poisoning and certain other consequences of external causes (S00-T88) (from D76)
  • neoplasms (C00-D49) (from D76)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D76)

Also known as

  • Reticulohistiocytoma (giant-cell)
  • Sinus histiocytosis with massive lymphadenopathy
  • Xanthogranuloma
  • Granuloma, reticulohistiocytic
  • Histiocytosis
  • Histiocytosis, lipid, lipoid
  • Histiocytosis, non-Langerhans cell
  • Histiocytosis, polyostotic sclerosing
  • Histiocytosis, sinus, with massive lymphadenopathy
  • Histiocytosis, syndrome NEC
  • Lipoid, histiocytosis
  • Reticulohistiocytoma
  • Syndrome, histiocytic
  • Syndrome, histiocytosis NEC

Parent code

  • D76Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissueHeader

Related codes

  • D76.1Hemophagocytic lymphohistiocytosisBillable
  • D76.2Hemophagocytic syndrome, infection-associatedBillable

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