Hemophagocytic syndrome, infection-associated
Billable / specific
D76.2 is a billable, specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes in FY2027.
Excludes1
Not coded here — never report together with this code.
- (Abt-) Letterer-Siwe disease (C96.0) (from D76)
- eosinophilic granuloma (C96.6) (from D76)
- Hand-Schüller-Christian disease (C96.5) (from D76)
- histiocytic medullary reticulosis (C96.9) (from D76)
- histiocytic sarcoma (C96.A) (from D76)
- histiocytosis X, multifocal (C96.5) (from D76)
- histiocytosis X, unifocal (C96.6) (from D76)
- Langerhans-cell histiocytosis, multifocal (C96.5) (from D76)
- Langerhans-cell histiocytosis NOS (C96.6) (from D76)
- Langerhans-cell histiocytosis, unifocal (C96.6) (from D76)
- leukemic reticuloendotheliosis (C91.4-) (from D76)
- lipomelanotic reticulosis (I89.8) (from D76)
- malignant histiocytosis (C96.A) (from D76)
- malignant reticulosis (C86.0) (from D76)
- nonlipid reticuloendotheliosis (C96.0) (from D76)
Excludes2
Not included here — may be reported together when both conditions exist.
- autoimmune disease (systemic) NOS (M35.9) (from D76)
- certain conditions originating in the perinatal period (P00-P96) (from D76)
- complications of pregnancy, childbirth and the puerperium (O00-O9A) (from D76)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) (from D76)
- endocrine, nutritional and metabolic diseases (E00-E88) (from D76)
- human immunodeficiency virus [HIV] disease (B20) (from D76)
- injury, poisoning and certain other consequences of external causes (S00-T88) (from D76)
- neoplasms (C00-D49) (from D76)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94) (from D76)
Use additional code
Add a code to identify the following, if applicable.
- code to identify infectious agent or disease.
Also known as
- Syndrome, hemophagocytic, infection-associated
- Syndrome, macrophage activation, due to infection
Parent code
- D76Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissueHeader